Cystic Fibrosis

Cystic fibrosis: • A disease of the exocrine glands: salivary, sweet, GI, pul • Rx: chest physio, Abx, bronchodilator, GI enzyme A→ sinusitis → avoid nasal intubation with active nasal infection. B→ pneumonia, mixed obstructive/restrictive disease, bronchiectasis C→ cor-pulmonale GI→ cholelithiasis, pancreatic insufficiency, hepatic dysfunction Heme→ bleeding disorder • Lab: CBC-D, lytes, BUN, creat, coags, CXR, PFT, ECG, Echo if needed • Monitors: CAS, art-line • Suction the airway before extubation • Consider regional block for post-op pain control • Encourage chest physio post-op