Valvular heart disease Tengku Winda Ardini, Sp.JP
CARDIAC ANATOMY AORTA
KATUP AORTA
ATRIUM KANAN
ATRIUM KIRI
KATUP TRICUSPID
KATUP MITRAL
ARTERI PULMONAL
VENTRIKEL KANAN
VENTRIKEL KIRI KATUP PULMONAL
CARDIAC VALVES
CARDIAC CYCLE
LA LV (Mitral Valve)
LV Aorta (Aortic Valve) RA RV (Tricuspid Valve) RV Arteri Pulmonal (Pulmonic Valve)
HEART SOUNDS (STETHOSCOPE)
S1 = Atrioventricular Valves closure
S2 = Semilunar valves closure
STENOSIS • Tidak terbuka secara penuh atau sempurna
REGURGITASI/INSUFISIENSI • Tidak tertutup secara penuh atau sempurna CARDIAC MURMUR
MITRAL STENOSIS
Symptoms: Fatique, shortness of breath, palpitation, swollen feet, chestpain, coughing of blood
Signs: cardiomegaly, cardiac murmur (mid diastolic murmur)
Etiology: Rheumatic heart disease
MITRAL STENOSIS Mid Diastolic Murmur Cardiomegaly, Pulmonal prominent, LA >, Apex upward
ECG: Sinus rhythm/ atrial fibrillation + Right axis deviation + right ventricular hypertrophy
MITRAL STENOSIS (TREATMENT) Medical therapy (Heart Failure) : Diuretics (furosemide, spironolactone), Rate control (beta blocker, digoxin), anticoagulant (if needed)
Ballon Mitral Valvuloplasty (BMV)
Surgery : Mitral Valve Replacement
MITRAL REGURGITASI
Symptoms: Fatique, shortness of breath, palpitation, swollen feet, chestpain
Signs: cardiomegaly, cardiac murmur (pan systolic murmur)
Etiology: Rheumatic heart disease, mitral valve prolapse, infective endocarditis, cardiomyopathy, ischemic heart disease
Pan Systolic Murmur
MITRAL REGURGITASI Cardiomegaly, LA >, LV >
ECG: Sinus rhythm/ atrial fibrillation + Left atrial enlargement / Left ventricular hypertrophy
MITRAL REGURGITATION (TREATMENT) Medical therapy (Heart Failure) : Diuretics (furosemide, spironolactone), Rate control (beta blocker), Ace inhibitor/Angiotensin receptor blocker, anticoagulant (if needed)
Surgery : Mitral Valve Repair / Replacement
AORTIC STENOSIS Symptoms: Fatique, shortness of breath, palpitation, fainting, chestpain, syncope.
Signs: cardiomegaly, cardiac murmur (ejection systolic murmur)
Etiology: Rheumatic heart disease, calcification, congenital (bicuspid valve)
AORTIC STENOSIS Ejection Systolic Murmur
ECG: Left atrial enlargement + Left ventricular hypertrophy + left ventricular strain
AORTIC STENOSIS (TREATMENT) Medical therapy (Heart Failure) : Diuretics (furosemide, spironolactone), beta blocker, statin, Renin angiotensin aldosterone blocker
Transcatheter Aortic Valve Implabtation (TAVI)
Surgery : Aortic Valve Replacement
AORTIC REGURGITATION Symptoms: Fatique, shortness of breath, palpitation, swollen feet, chestpain.
Signs: cardiomegaly, cardiac murmur (early diastolic murmur), 14 signs
Etiology: Rheumatic heart disease, calcification, congenital, aortic root disease, connective tissue disease
14 SIGS AORTIC REGURGITATION •
CORRIGAN’S PULSE: A RAPID AND FORCEFUL DISTENSION OF THE ARTERIAL PULSE WITH A QUICK COLLAPSE
•
DE MUSSET’S SIGN: BOBBING OF THE HEAD WITH EACH HEARTBEAT (LIKE A BIRD WALKING)
•
MULLER’S SIGN: VISIBLE PULSATIONS OF THE UVULA
•
QUINCKE’S SIGN: CAPILLARY PULSATIONS SEEN ON LIGHT COMPRESSION OF THE NAIL BED
•
TRAUBE’S SIGN: SYSTOLIC AND DIASTOLIC SOUNDS HEARD OVER THE FEMORAL ARTERY (“PISTOL SHOTS”)
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DUROZIEZ’S SIGN: GRADUAL PRESSURE OVER THE FEMORAL ARTERY LEADS TO A SYSTOLIC AND DIASTOLIC BRUIT
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HILL’S SIGN: POPLITEAL SYSTOLIC BLOOD PRESSURE EXCEEDING BRACHIAL SYSTOLIC BLOOD PRESSURE BY ≥ 60 MMHG (MOST SENSITIVE SIGN FOR AORTIC REGURGITATION)
•
SHELLY’S SIGN: PULSATION OF THE CERVIX
•
ROSENBACH’S SIGN: HEPATIC PULSATIONS
•
BECKER’S SIGN: VISIBLE PULSATION OF THE RETINAL ARTERIOLES
•
GERHARDT’S SIGN (AKA SAILER’S SIGN): PULSATION OF THE SPLEEN IN THE PRESENCE OF SPLENOMEGALY
•
MAYNE’S SIGN: A DECREASE IN DIASTOLIC BLOOD PRESSURE OF 15 MMHG WHEN THE ARM IS HELD ABOVE THE HEAD (VERY NON-SPECIFIC)
•
LANDOLFI’S SIGN: SYSTOLIC CONTRACTION AND DIASTOLIC DILATION OF THE PUPIL
AORTIC REGURGITATION Early Diastolic Murmur
PULMONARY STENOSIS Symptoms: Fatique, shortness of breath, sianosis. Signs: cardiomegaly, cardiac murmur (ejection systolic murmur)
Etiology : congenital
PULMONARY REGURGITATION
Etiology : pulmonary hypertension
TRICUSPID REGURGITATION Symptoms: Fatique, shortness of breath. Signs: cardiomegaly, cardiac murmur (systolic murmur) Etiology : pulmonary hypertention, rheumatic heart disease
TRICUSPID STENOSIS
ETIOLOGY
ETIOLOGY
RHEUMATIC HEART DISEASE • Streptococcus Beta Haemolytic group A infection throat (pharynx) pharyngitis Rheumatic Fever • Several episodes • Autoimmun inflammatory reaction • Children and young adult • Low - middle income countries, marginal communities in high income countries.
ECHOCARDIOGRAPHY VENTRIKEL KANAN
KATUP TRICUSPID
VENTRIKEL KIRI
KATUP MITRAL
VENTRIKEL KANAN ATRIUM KIRI
TERIMA KASIH
FIGURE 2. THERAPEUTIC ROLES OF RENINANGIOTENSIN-ALDOSTERONE SYSTEM INHIBITION IN AORTIC STENOSIS.
FIGURE 1. THERAPEUTIC ROLES OF STATINS AND OTHER LIPID-LOWERING THERAPY IN AORTIC STENOSIS.