Diseases Of Infancy And Childhood Ii

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DISEASES OF INFANCY & CHILDHOOD II R. HUGO MARTÍNEZ LOZANO, M.D. Aug-31-2009.

LEARNING OBJECTIVES: K & U ABOUT SOME INBORN ERRORS OF METABOLISM - PKU - GALACTOSEMIA - CF  SIDS  BENIGN NEOPLASIAS - HEMANGIOMAS & LYMPHANGIOMAS - TERATOMAS - CONGENITAL NEVI  MALIGNANT NEOPLASIAS - INCIDENCE & TYPES (REVIEW OF THE M.I.) - THE NEUROBLASTIC TUMORS - WILM’S TUMOR Ref: pp. 487-506 & lecture’s information 

CYSTIC FIBROSIS (MUCOVISCIDOSIS)

NEOPLASMS  -

BENIGN: HEMANGIOMAS LYMPHANGIOMA TERATOMAS CONGENITAL NEVI

HEMANGIOMA: PHENOMENON?

IDEM

CONGENITAL NEVI

MALIGNANT TUMORS: INCIDENCE & TYPES: 0-4 YEARS

LEUKEMIA RETINOBLASTOMA NEUROBLASTOMA WILMS TUMOR HEPATOBLASTOMA SARCOMAS TERATOMAS MEDULLOBLASTOMA

5-9 YEARS

LEUKEMIA RETINOBLASTOMA NEUROBLASTOMA HEPATOCA. SARCOMAS MEDULLO/ASTRO EWING SARCOMA LYMPHOMA

10-14 YEARS

HEPATOCA. SARCOMAS OSTEOSARCOMA THYROID CA HODGKIN DIS.

Genetic basis (& markers) of some pediatric neoplasias 

Table 10-10, pag. 500.

ALL

THE NEUROBLASTIC TUMORS

Wilms’ tumor (nephroblastoma)

IDEM

HEPATOBLASTOMA

EWING’S SARCOMA

SYMPTOMS? MAIN SIGN? TOPOGRAPHY OF THE LESION? MOST LIKELY NATURE OF IT?

Describe it Name of the shown clue… Homer-Wright rosettes

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